The lymphoproliferative auto-immune syndrome: a rare cause of peripheral cytopenia
Raida Ben Salah 1 * , Mona Snoussi 1, Nour Louati 2, Chebbi Donia 1, Faten Frikha 1, Mnif Hela 2, Bahloul Zouhir 1
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1 Department of Internal Medicine, Hedi Chaker Hospital Sfax, Tunisia
2 Center of Transfusion, Hedi Chaker Hospital Sfax, Tunisia
* Corresponding Author


Autoimmune Lymphoproliferative syndrome is an inherited disorder manifesting with autoimmune cytopenia, lymphadenopathy and splenomegaly. The differential diagnosis includes infections, autoimmune disorders or malignancies. The disease is characterized by accumulation of double negative (CD3+ CD4- CD8-) T cells (DNT) in the peripheral blood. Here we report the case of 19 years-old girl that was diagnosed as autoimmune Lymphoproliferative syndrome with a literature review.


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Article Type: Case Report

ELECTRON J GEN MED, 2018 - Volume 15 Issue 5, Article No: em78

Publication date: 23 Aug 2018

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Article Downloads: 819

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