Atypical fibroxanthoma (AFX) is probably a neoplasm of fibrohistiocytic lineage. The tumor arise in the skin and has strikingly atypical properties. We report a case of AFX that was excised from the left lower eyelid of a twelve-year-old girl. The nodular mass was reported as AFX. Though this tumor has the capability to recur aggresively, no recurrence was noted in the present case. Malignant fibrous histiocytoma, atypical fibrous histiocytoma, squamous cell carcinoma, sarcoma, dermatofibroma protuberans, and reticulohistiocytoma should be included in differential diagnosis.