A Rare Vasculitis of Childhood, Takayasu Arteritis
Aydın Ece 1 * , Velat Şen 1, Sevgi Yavuz 1, Ali Güneş 1, Ünal Uluca 1, Cahit Şahin 1
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1 Dicle University Medical School, Department of Pediatrics, Diyarbakır, Turkey
* Corresponding Author

Abstract

Takayasu arteritis is a potentially life threatening vasculitis that characterized by granulomatous inflammation of large vessels including aorta, its major branches and pulmonary arteries. True incidence of TA is not known in children, since TA is very rare; however, incidence of TA has been estimated as 0.8-2.6 per million children. Making a diagnosis is more difficult in childhood compared with adults due to non-specific clinical findings. The diagnosis of TA is done based on clinical criteria, laboratory investigations support and radiologic images confirm the diagnosis. Corticosteroids with other immunosuppressive drugs are used for treatment and biological agents are given to resistant cases. In this report, it was aimed to draw attention to a potentially fatal disease that frequently diagnostic delays and therapeutic difficulties occur. We, herein reported signs, symptoms, imaging methods and treatment modalities of two children, a 12 year-old male and a 13 year-old female patients, that presented with non-specific initial symptoms and diagnosed as TA with clinical findings and radiological images.

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This is an open access article distributed under the Creative Commons Attribution License which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Article Type: Case Report

https://doi.org/10.29333/ejgm/82349

EUR J GEN MED, 2013 - Volume 10 Issue Supplement 1, pp. 98-102

Publication date: 09 Jan 2013

Article Views: 723

Article Downloads: 406

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