Hypothalamic hamartoma is a developmental malformation in the region of tuber cinereum and mamillary bodies. It presents the most commonly detectable lesion in patients with precocious puberty and is associated with gelastic seizures. As well as, it can be completely silent to be found only incidentally. Computed tomography (CT) and magnetic rezonans (MR) imaging are preferred imaging modalities in diagnose of hypothalamic hamartomas. The aim of this study is to present the radiologic imaging findings of a rare hypothalamic hamartoma case.