The lymphoproliferative auto-immune syndrome: a rare cause of peripheral cytopenia
Raida Ben Salah 1 * , Mona Snoussi 1, Nour Louati 2, Chebbi Donia 1, Faten Frikha 1, Mnif Hela 2, Bahloul Zouhir 1
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1 Department of Internal Medicine, Hedi Chaker Hospital Sfax, Tunisia
2 Center of Transfusion, Hedi Chaker Hospital Sfax, Tunisia
* Corresponding Author

Abstract

Autoimmune Lymphoproliferative syndrome is an inherited disorder manifesting with autoimmune cytopenia, lymphadenopathy and splenomegaly. The differential diagnosis includes infections, autoimmune disorders or malignancies. The disease is characterized by accumulation of double negative (CD3+ CD4- CD8-) T cells (DNT) in the peripheral blood. Here we report the case of 19 years-old girl that was diagnosed as autoimmune Lymphoproliferative syndrome with a literature review.

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This is an open access article distributed under the Creative Commons Attribution License which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Article Type: Case Report

https://doi.org/10.29333/ejgm/94112

Electron J Gen Med, 2018 - Volume 15 Issue 5, Article No: em78

Publication date: 23 Aug 2018

Article Views: 227

Article Downloads: 54

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