Telescopic Aortic Arch: A New Entity in Marfan Syndrome
Muhammet Mustafa Arslan 1, Ramazan Akçan 2, Ismail Zararsız 3, Sedat Meydan 3
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1 Mustafa Kemal University Medical Faculty Department of Forensic Medicine, Hatay, Turkey
2 Dicle University Faculty of Medicine Department of Forensic Medicine, Diyarbakır, Turkey
3 Mustafa Kemal University Medical Faculty Department of Anatomy, Hatay, Turkey

Abstract

Telescopic aortic arch is a consequence of aortic dissection in Marfan’s syndrome, which has not been reported previously. This paper presents the first case of telescopic aortic arch secondary to chronic aortic dissection, as an incidental finding of a forensic autopsy. Here we present a sudden death of a 20 years old male due to cardiac tamponade sourcing from the rupture of ascending aorta. At autopsy, there was a haemopericardium of 800 cc, which comprised blood and clot. The ascending thoracic aorta was dilated and a 1.2 cm ragged linear complete rupture was noticed on the medial side of the front wall of ascending aorta. Examination of aorta showed a second/inner aortic arch just as a tube lying inside the aortic arch. The inner aortic arch was arrised 2.5 cm above aortic valves and lasted at the beginning of the descending aorta. It was 10 cm in length with a lumen 2 cm in diameter and was associated with truncus brachiosephalicus, left common carotid, and left subclavian arteries.

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This is an open access article distributed under the Creative Commons Attribution License which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

Article Type: Case Report

https://doi.org/10.29333/ejgm/82745

Eur J Gen Med, 2011 - Volume 8 Issue 3, pp. 236-239

Publication date: 11 Jul 2011

Article Views: 64

Article Downloads: 19

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