Constipation is the group of disease that is most frequently consulted with experts in pediatric gastroenterology. Abnormal neurological examination, non-intestinal symptoms or cases unresponsive to treatment should be stimulative and suggestive of another underlying cause to the doctor. Mature B-cell malignant disease (Burkitt lymphoma) forms 35-40 % of all non-Hodgkin lymphoma patients. Burkitt lymphoma can be a mass in gastrointestinal system. In this paper, a four-year-old boy who was hospitalized for 17 days in other centers with a diagnosis of malnutrition and constipation and diagnosed as primary intestinal lymphoma in our clinic is presented. Primary intestinal lymphomas discussed under the light of literature.